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심정지로 응급실에 내원한 부정맥야기성 우심실이형성/심근병증 1례
A Case of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy with Cardiac Arrest in the Emergency Department

대한응급의학회지 2006년 17권 6호 p.646 ~ p.651

양희범(Yang Hee-Bum) - 을지대학교 의과대학 응급의학교실
성원영(Sung Won-Young) - 을지대학교 의과대학 응급의학교실
박현욱(Park Hyun-Wook) - 을지대학교 의과대학 응급의학교실
이장영(Lee Jang-Young) - 을지대학교 의과대학 응급의학교실
홍성엽(Hong Sung-Youp) - 을지대학교 의과대학 응급의학교실
양영모(Yang Young-Mo) - 을지대학교 의과대학 응급의학교실

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a heart muscle disorder characterized by patch replacement of right ventricular myocardium by adipose and fibrous tissue and by electrical instability of the right ventricular myocardium. ARVD/C is rare in South Korea but is an important cause of cardiac arrest in young patients. The clinical manifestations of ARVD/C vary from sudden cardiac death of previously asymptomatic patients to chronic symptoms in patients with recurrent palpitations and/or right or biventricular failure. Diagnosis is based on several major and minor criteria involving structural, histologic, eletrocardiographic, arrhythmic, and genetic factors. Therapy is directed to prevent and/or treat malignant vetricular tachyarrhythmias with medications, implantable cadioverter defibrillator, radiofrequency ablation, and surgery in selected cases. We experienced a case of ARVD/C with ventricular fibrilltion in the emergency department. The electrocardiography of postresuscitation showed QRS prolongation and inversion of T waves in the right precordial leads. Echocardiography revealed a dilated right atrium and right ventricle, and right ventricular dysfunction. Multislice computed tomography and cardiac magnetic resonance imaging showed multifocal fat infiltration involving right ventricular myocardium, right ventricular trabeulae, and the right ventricular side of the ventricular septum with dilatation of the right ventricle and right ventricular outflow tract and abundant epicardial fat. An implantable cardioverter defibrillator was implanted, and the patient was transferred to another hospital.

키워드

Arrhythmogenic right ventricular dysplasia, Cardiomyopathy, Ventricular fibrillation, Cardiac arrest

KMID : 0385920060170060646

원문 및 링크아웃 정보

등재저널 정보

주제코드

주제명(Target field)

연구대상(Population)

연구참여(Sample size)

대상성별(Gender)

질병특성(Condition Category)

연구환경(Setting)

연구설계(Study Design)

연구기간(Period)

중재방법(Intervention Type)

중재명칭(Intervention Name)

키워드(Keyword)

유효성결과(Recomendation)

An implantable cardioverter defibrillator was implanted, and the patient was transferred to another hospital.

연구비지원(Fund Source)

근거수준평가(Evidence Hierarchy)

출판년도(Year)

참여저자수(Authors)

대표저자

DOI

KCD코드

ICD 03

건강보험코드

심정지로 응급실에 내원한 부정맥야기성 우심실이형성/심근병증 1례 A Case of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy with Cardiac Arrest in the Emergency Department

Abstract

키워드

심정지로 응급실에 내원한 부정맥야기성 우심실이형성/심근병증 1례
A Case of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy with Cardiac Arrest in the Emergency Department